Interstitial Lung Diseases
Idiopathic pulmonary fibrosis (IPF)
Idiopathic interstitial pneumonia (IIP)
Organizing pneumonia (OP)
Acute eosinophilic pneumonia
Chronic eosinophilic pneumonia
Sarcoidosis
Rheumatoid arthritis (RA-ILD)
Systemic sclerosis (SSc-ILD)
Mixed connective tissue disease (MCTD-ILD)
Idiopathic inflammatory myopathies (IIM-ILD)
Anti-synthetase syndrome (ASyS-ILD)
Other SARD-ILD
Hypersensitivity pneumonitis (HP)
Pneumoconiosis
Smoking-related ILD
Other substance/drug-induced ILD
Bronchiolitis & adjacent disease
Morphologic Patterns
(Imaging & Histopathologic)
Usual interstitial pneumonia (UIP)
Non-specific interstitial pneumonia (NSIP)
Bronchiolocentric interstitial pneumonia (BIP)
Diffuse alveolar damage (DAD)
Pleuroparenchymal fibroelastosis (PPFE)
Lymphoid interstitial pneumonia (LIP)
Organizing pneumonia (OP)
Respiratory-bronchiolitis ILD (RB-ILD)
Alveolar macrophage pneumonia (AMP)
Acute eosinophilic pneumonia (AEP)
Chronic eosinophilic pneumonia (CEP)
Other rare alveolar filling disorders
Combined pattern
Unclassifiable pattern
Cyst-predominant pattern
Descriptors & Other Key Terms
Interstitial Pneumonia with Autoimmune Features (IPAF)
Acute respiratory worsening (ARW)
Acute exacerbation of fibrotic ILD (AE-fILD)
Rapidly progressive ILD (RP-ILD)
Combined Pulmonary Fibrosis & Emphysema (CPFE)